Development of new classification criteria for macrophage activation syndrome complicating systemic juvenile idiopathic arthritis
نویسندگان
چکیده
Development of new classification criteria for macrophage activation syndrome complicating systemic juvenile idiopathic arthritis Francesca Minoia, Sergio Davì, Francesca Bovis, Angela Pistorio, Maurizio Aricò, Tadej Avcin, Ed Behrens, Fabrizio De Benedetti, Lisa Filipovich, Alexei Grom, Jan-Inge Henter, AnnaCarin Horne, Norman Ilowite, Michael Jordan, Raju Khubchandani, Toshiyuki Kitoh, Kai Lehmberg, Dan Lovell, Paivi Miettunen, Kim Nichols, Jana Pachlopnik, Seza Ozen, Athimalaipet V. Ramanan, Ricardo Russo, Rayfel Schneider, Gary Sterba, Carol Wallace, Carine Wouters, Nico Wulffraat, Yosef Uziel, Nicola Ruperto, Alberto Martini, Randy Q Cron, Angelo Ravelli
منابع مشابه
Macrophage Activation Syndrome as the First Presentation of Juvenile Idiopathic Arthritis
Macrophage activation syndrome (MAS) is a rare feature of rheumatic disorders in children and adolescence and its presentation as the first symptom of rheumatic disorders is very infrequent. A 9-year-old girl, in whom MAS developed, was admitted to our Hospital in Tehran, Iran. She suffered from high grade fever and rash followed by multiple joint swelling months afterwards. Bone marrow aspira...
متن کاملMacrophage activation syndrome presenting with pericardial effusion, hyponatremia and renal involvement.
BACKGROUND Macrophage activation syndrome is a rare and life threatening complication of childhood rheumatic disorders. CASE CHARACTERISTICS 6-year-old male child with macrophage activation syndrome complicating systemic onset juvenile idiopathic arthritis. OBSERVATION He developed pericardial effusion, hyponatremia and deranged renal function. OUTCOME Improvement on intravenous cortico s...
متن کاملSensitivity and specificity of current diagnostic guidelines in children with macrophage activation syndrome complicating systemic juvenile idiopathic arthritis
Background Early diagnosis of macrophage activations syndrome (MAS) in systemic juvenile idiopathic arthritis (sJIA) may be challenging because it may mimic the clinical features of the underlying disease or be confused with an infectious complication. However, the diagnostic value of the guidelines for hemophagocytic lymphohistiocytosis (HLH) (1) or sJIA-associated MAS (2) has seldom been exam...
متن کاملShould 2016 Criteria for Macrophage Activation Syndrome be applied in children with Kawasaki disease, as well as with systemic-onset juvenile idiopathic arthritis?
We read with deep interest the paper by Ravelli et al, who developed new criteria for the classification of macrophage activation syndrome (MAS) in patients with systemic-onset juvenile idiopathic arthritis (So-JIA). The hemophagocytic lymphohistiocytosis (HLH) diagnostic guidelines have been successfully used in the management of primary HLH, but there have been several limitations to their us...
متن کاملA case of systemic juvenile idiopathic arthritis with pulmonary hemosiderosis secondary to recurrent macrophage activation syndrome or a new autoinflammatory syndrome?
Introduction Macrophage activation syndrome (MAS), a severe complication of systemic juvenile idiopathic arthritis (JIA) and other inflammatory diseases, represents a one of the most important rheumatological emergencies. Delayed diagnosis could lead to life-threatening complications. Pulmonary hemosiderosis (PH), possible seen at all ages but most commonly among children, usually appears as an...
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عنوان ژورنال:
دوره 12 شماره
صفحات -
تاریخ انتشار 2014